ADAMTS19

ADAM metallopeptidase with thrombospondin type 1 motif 19
OMIM: 607513, Gene2Phenotype

4 panels

Panel Reviews Mode of inheritance Details
4 panels
Green ADAMTS19 in Familial non syndromic congenital heart disease

Level 3: Congenital heart disease
Level 2: Cardiovascular disorders
Version 1.90

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Literature
Phenotypes
  • Non-syndromic heart valve disease
  • heart valve disease, MONDO:0002869
Amber ADAMTS19 in Fetal anomalies


Level 2: Fetal (including NIPD)
Version 6.185
Latest signed off version: v6.0 (30 Apr 2025)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • NHS GMS
  • Expert Review Amber
Phenotypes
  • Cardiac valvular dysplasia 2, OMIM:620067
Green ADAMTS19 in DDG2P


Version 6.447
Latest signed off version: v6.0 (30 Apr 2025)

Component of the following Super Panels:

  • Paediatric disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • DD-Gene2Phenotype
    • Expert Review Green
    Phenotypes
    • OMIM:620067.0
    • MONDO:0859572
    • ADAMTS19-related cardiac valvular dysplasia
    Green ADAMTS19 in Paediatric disorders - additional genes


    Level 2: Developmental disorders
    Version 7.41
    Latest signed off version: v7.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • NHS GMS
    • Expert Review Green
    • Literature
    Phenotypes
    • Non-syndromic heart valve disease
    • heart valve disease, MONDO:0002869