ADAMTS3

ADAM metallopeptidase with thrombospondin type 1 motif 3
OMIM: 605011, Gene2Phenotype

3 panels

Panel Reviews Mode of inheritance Details
3 panels
Green ADAMTS3 in Intestinal failure or congenital diarrhoea


Level 2: Gastrohepatology
Version 3.7
Latest signed off version: v3.0 (22 Mar 2023)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
Phenotypes
  • Hennekam lymphangiectasia-lymphedema syndrome 3, OMIM:618154
Green ADAMTS3 in Fetal anomalies


Level 2: Fetal (including NIPD)
Version 6.140
Latest signed off version: v6.0 (30 Apr 2025)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Literature
Phenotypes
  • Hennekam lymphangiectasia-lymphedema syndrome 3, OMIM:618154
  • Hennekam lymphangiectasia-lymphedema syndrome 3, MONDO:0032564
Green ADAMTS3 in Primary lymphoedema


Level 2: Cardiology
Version 4.21
Latest signed off version: v4.0 (30 Apr 2025)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Expert list
  • London South GLH
  • UKGTN
  • Other
Phenotypes
  • Hennekam lymphangiectasia-lymphedema syndrome 3, OMIM:618154
  • Hennekam lymphangiectasia-lymphedema syndrome 3, MONDO:0032564