ATP2A2

ATPase sarcoplasmic/endoplasmic reticulum Ca2+ transporting 2
OMIM: 108740, Gene2Phenotype

4 panels

Panel Reviews Mode of inheritance Details
4 panels
Amber ATP2A2 in Rhabdomyolysis and metabolic muscle disorders


Level 2: Neurology
Version 5.14
Latest signed off version: v5.4 (30 Apr 2025)

Component of the following Super Panels:

  • Hypotonic infant
  • Other rare neuromuscular disorders
  • review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • Expert Review Amber
    • Literature
    Phenotypes
    • Dominant rhabdomyolysis
    Tags
    • Q1_25_ promote_green
    Amber ATP2A2 in Epidermolysis bullosa and congenital skin fragility


    Level 2: Dermatology
    Version 2.13
    Latest signed off version: v2.2 (22 Mar 2023)

    review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Amber
    Phenotypes
    • Darier disease, OMIM:124200
    • Acrokeratosis verruciformis, OMIM:101900
    • Darier disease, MONDO:0007417
    • acrokeratosis verruciformis, MONDO:0007048
    Tags
    • Q1_26_promote_green
    • Q1_26_NHS_review
    Green ATP2A2 in Mosaic skin disorders - deep sequencing


    Level 2: Dermatology
    Version 3.27
    Latest signed off version: v3.0 (30 Apr 2025)

    review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • NHS GMS
    • Expert Review Green
    Phenotypes
    • Segmental Darier disease OMIM:124200
    • Darier-White disease OMIM:124200
    • Acrokeratosis verruciformis, OMIM:101900
    Red ATP2A2 in Intellectual disability


    Level 2: Developmental disorders
    Version 9.285
    Latest signed off version: v9.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • Expert Review Red
    • Radboud University Medical Center, Nijmegen
    Phenotypes
    • Darier disease 124200