BLOC1S5

biogenesis of lysosomal organelles complex 1 subunit 5
OMIM: 607289, Gene2Phenotype

3 panels

Panel Reviews Mode of inheritance Details
3 panels
Green BLOC1S5 in Albinism or congenital nystagmus


Level 2: Ophthalmology
Version 4.2
Latest signed off version: v4.0 (30 Apr 2025)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • NHS GMS
Phenotypes
  • Hermansky-Pudlak syndrome, MONDO:0019312
Green BLOC1S5 in Bleeding and platelet disorders


Level 2: Haematology
Version 4.6
Latest signed off version: v4.0 (30 Apr 2025)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • NHS GMS
  • Expert Review Green
  • Literature
Phenotypes
  • Hermansky–Pudlak syndrome 11, OMIM:619172
  • Hermansky-Pudlak syndrome 11, MONDO:0030903
Red BLOC1S5 in Monogenic hearing loss


Level 2: Audiology
Version 5.57
Latest signed off version: v5.0 (30 Apr 2025)

Component of the following Super Panels:

  • Paediatric disorders
  • review Unknown
    Sources
    • Expert list