DLX5

distal-less homeobox 5
OMIM: 600028, Gene2Phenotype

5 panels

Panel Reviews Mode of inheritance Details
5 panels
Green DLX5 in Limb disorders


Level 2: Musculoskeletal
Version 7.20
Latest signed off version: v7.0 (30 Apr 2025)

Component of the following Super Panels:

  • Paediatric disorders
  • review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
    Sources
    • NHS GMS
    • Expert list
    • Expert Review Green
    • London South East RGC GSTT
    • Viapath
    Phenotypes
    • ?Split-hand/foot malformation 1 with sensorineural hearing loss, OMIM:220600
    • Split-hand/foot malformation 1, OMIM:183600
    Green DLX5 in Skeletal dysplasia


    Level 2: Musculoskeletal
    Version 8.34
    Latest signed off version: v8.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
    Sources
    • NHS GMS
    • Expert Review Green
    • Expert list
    Phenotypes
    • ?Split-hand/foot malformation 1 with sensorineural hearing loss, OMIM:220600
    • Split-hand/foot malformation 1, OMIM:183600
    Green DLX5 in Fetal anomalies


    Level 2: Fetal (including NIPD)
    Version 6.140
    Latest signed off version: v6.0 (30 Apr 2025)

    review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • Expert list
    Phenotypes
    • ?Split-hand/foot malformation 1 with sensorineural hearing loss, 220600
    • Split-hand/foot malformation 1, 183600
    Red DLX5 in DDG2P


    Version 6.424
    Latest signed off version: v6.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • DD-Gene2Phenotype
    • Expert Review Red
    Phenotypes
    • SPLIT HAND AND FOOT MALFORMATION 220600
    Red DLX5 in Monogenic hearing loss


    Level 2: Audiology
    Version 5.57
    Latest signed off version: v5.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • review Not set
    Sources
    • Expert