IKBKE

inhibitor of nuclear factor kappa B kinase subunit epsilon
OMIM: 605048, Gene2Phenotype

2 panels

Panel Reviews Mode of inheritance Details
2 panels
Amber IKBKE in Primary immunodeficiency or monogenic inflammatory bowel disease


Level 2: Immunology
Version 9.102
Latest signed off version: v9.91 (12 Aug 2026)

review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Amber
  • Literature
Phenotypes
  • Herpes Simplex Virus type 2 (HSV-2) meningitis
  • autoinflammatory syndrome, MONDO:0019751
Amber IKBKE in Autoinflammatory disorders


Level 2: Immunology
Version 3.21
Latest signed off version: v3.16 (12 Aug 2026)

review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Literature
  • Expert Review Amber
Phenotypes
  • Herpes Simplex Virus type 2 (HSV-2) meningitis
  • autoinflammatory syndrome, MONDO:0019751