ISCA-37417-Loss

3 panels

Panel Reviews Mode of inheritance Details
3 panels
Green ISCA-37417-Loss Region in Autosomal recessive congenital ichthyosis

Level 3: Ichthyoses
Level 2: Dermatological disorders
Version 1.15

review X-LINKED: hemizygous mutation in males, biallelic mutations in females
Sources
  • Expert Review Green
  • ClinGen
Phenotypes
  • Ichthyosis, X-linked
  • 308100
Green ISCA-37417-Loss Region in Ichthyosis and erythrokeratoderma


Level 2: Dermatology
Version 4.16
Latest signed off version: v4.0 (30 Apr 2025)

review X-LINKED: hemizygous mutation in males, biallelic mutations in females
Sources
  • Expert Review Green
Phenotypes
  • Ichthyosis, X-linked, OMIM:308100
  • ichthyosis, MONDO:0019269
Amber ISCA-37417-Loss Region in Proteinuric renal disease


Level 2: Renal
Version 6.13
Latest signed off version: v6.0 (6 May 2026)

Component of the following Super Panels:

  • Unexplained young onset end-stage renal disease
  • review X-LINKED: hemizygous mutation in males, biallelic mutations in females
    Sources
    • Expert Review Amber
    • Literature
    Phenotypes
    • Ichthyosis, X-linked, OMIM:308100
    • ichthyosis, MONDO:0019269
    Tags
    • Q3_26_expert_review
    • Q3_26_promote_green