KDELR2

KDEL endoplasmic reticulum protein retention receptor 2
OMIM: 609024, Gene2Phenotype

4 panels

Panel Reviews Mode of inheritance Details
4 panels
Green KDELR2 in Skeletal dysplasia


Level 2: Musculoskeletal
Version 8.39
Latest signed off version: v8.0 (30 Apr 2025)

Component of the following Super Panels:

  • Paediatric disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • Literature
    Phenotypes
    • Osteogenesis imperfecta, type XXI, OMIM:619131
    • Increased susceptibility to fractures
    • Joint hypermobility
    • Scoliosis
    • Bowing of the legs and arms
    Green KDELR2 in Fetal anomalies


    Level 2: Fetal (including NIPD)
    Version 6.183
    Latest signed off version: v6.0 (30 Apr 2025)

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • NHS GMS
    Phenotypes
    • Osteogenesis imperfecta, type XXI, OMIM:619131
    Green KDELR2 in Osteogenesis imperfecta


    Level 2: Musculoskeletal
    Version 5.5
    Latest signed off version: v5.0 (30 Apr 2025)

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • Literature
    Phenotypes
    • Osteogenesis imperfecta, type XXI, OMIM:619131
    • Increased susceptibility to fractures
    • Joint hypermobility
    • Scoliosis
    • Bowing of the legs and arms
    Green KDELR2 in DDG2P


    Version 6.447
    Latest signed off version: v6.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • DD-Gene2Phenotype
    • Expert Review Green
    Phenotypes
    • KDELR2-related Osteogenesis Imperfecta