KRT6A

keratin 6A
OMIM: 148041, Gene2Phenotype

2 panels

Panel Reviews Mode of inheritance Details
2 panels
Green KRT6A in Palmoplantar keratoderma and erythrokeratodermas

Level 3: Keratodermas
Level 2: Dermatological disorders
Version 1.35

review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
  • Radboud University Medical Center, Nijmegen
  • UKGTN
  • Eligibility statement prior genetic testing
Phenotypes
  • Pachyonychia congenital
  • Pachyonychia Congenita, Type 1
  • Pachyonychia congenita, Jadassohn-Lewandowsky type, 167200
Green KRT6A in Ichthyosis and erythrokeratoderma


Level 2: Dermatology
Version 4.9
Latest signed off version: v4.0 (30 Apr 2025)

review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Green
Phenotypes
  • Pachyonychia congenita 3, OMIM:615726