P4HA1

prolyl 4-hydroxylase subunit alpha 1
OMIM: 176710, Gene2Phenotype

3 panels

Panel Reviews Mode of inheritance Details
3 panels
Red P4HA1 in Arthrogryposis


Level 2: Neurology
Version 10.9
Latest signed off version: v10.0 (6 May 2026)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Red
  • Literature
Phenotypes
  • connective tissue disorder, MONDO:0003900
Red P4HA1 in Congenital myopathy


Level 2: Neurology
Version 7.46
Latest signed off version: v7.0 (6 May 2026)

Component of the following Super Panels:

  • Hypotonic infant
  • Other rare neuromuscular disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Red
    • Literature
    Phenotypes
    • connective tissue disorder, MONDO:0003900
    Red P4HA1 in Ehlers Danlos syndrome with a likely monogenic cause


    Level 2: Musculoskeletal
    Version 4.13
    Latest signed off version: v4.0 (30 Apr 2025)

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Red
    • Literature
    Phenotypes
    • connective tissue disorder, MONDO:0003900