RNU5A-1

RNA, U5A small nuclear 1
OMIM: 180691, Gene2Phenotype

3 panels

Panel Reviews Mode of inheritance Details
3 panels
Amber RNU5A-1 in Fetal anomalies


Level 2: Fetal (including NIPD)
Version 6.140
Latest signed off version: v6.0 (30 Apr 2025)

review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Amber
Phenotypes
  • Neurodevelopmental disorder, MONDO:0700092
Red RNU5A-1 in Early onset or syndromic epilepsy


Level 2: Neurology
Version 8.120
Latest signed off version: v8.0 (30 Apr 2025)

Component of the following Super Panels:

  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • Literature
    • Expert Review Red
    Phenotypes
    • Neurodevelopmental disorder, MONDO:0700092
    Tags
    • locus-type-rna-small-nuclear
    Red RNU5A-1 in Intellectual disability


    Level 2: Developmental disorders
    Version 9.279
    Latest signed off version: v9.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • Expert Review Red
    • Literature
    Phenotypes
    • Neurodevelopmental disorder, MONDO:0700092
    Tags
    • locus-type-rna-small-nuclear