UBR5

ubiquitin protein ligase E3 component n-recognin 5
OMIM: 608413, Gene2Phenotype

3 panels

Panel Reviews Mode of inheritance Details
3 panels
Green UBR5 in DDG2P


Version 6.424
Latest signed off version: v6.0 (30 Apr 2025)

Component of the following Super Panels:

  • Paediatric disorders
  • review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • DD-Gene2Phenotype
    • Expert Review Green
    Phenotypes
    • UBR5-related neurodevelopmental disorder
    • MONDO:0700092
    Amber UBR5 in Early onset or syndromic epilepsy


    Level 2: Neurology
    Version 8.125
    Latest signed off version: v8.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Amber
    • Literature
    Phenotypes
    • complex neurodevelopmental disorder, MONDO:0100038
    Tags
    • dd_review
    • Q3_25_promote_green
    Amber UBR5 in Intellectual disability


    Level 2: Developmental disorders
    Version 9.285
    Latest signed off version: v9.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Amber
    • Literature
    Phenotypes
    • complex neurodevelopmental disorder, MONDO:0100038
    Tags
    • dd_review
    • Q3_25_promote_green