UNC13A

unc-13 homolog A
OMIM: 609894, Gene2Phenotype

6 panels

Panel Reviews Mode of inheritance Details
6 panels
Amber UNC13A in Congenital myaesthenic syndrome


Level 2: Neurology
Version 5.7
Latest signed off version: v5.0 (30 Apr 2025)

Component of the following Super Panels:

  • Hypotonic infant
  • Other rare neuromuscular disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Amber
    • NHS GMS
    • Wessex and West Midlands GLH
    Phenotypes
    • congenital myasthenic syndrome, MONDO:0018940
    Tags
    • Q4_25_promote_green
    • Q4_25_NHS_review
    Red UNC13A in Adult onset neurodegenerative disorder


    Level 2: Neurology
    Version 8.11
    Latest signed off version: v8.0 (30 Apr 2025)

    review Unknown
    Sources
    • Expert Review Red
    Red UNC13A in Amyotrophic lateral sclerosis/motor neuron disease

    Level 3: Neurodegenerative disorders
    Level 2: Neurology and neurodevelopmental disorders
    Version 1.74

    review Unknown
    Sources
    • Literature
    Green UNC13A in DDG2P


    Version 6.424
    Latest signed off version: v6.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
    Sources
    • DD-Gene2Phenotype
    • Expert Review Green
    Phenotypes
    • UNC13A-related congenital epileptic encephalopathy and severe neuromuscular disorder
    • MONDO:0100038
    • UNC13A-related neurodevelopmental disorder with ataxia and tremor or dyskinetic movements
    Amber UNC13A in Early onset or syndromic epilepsy


    Level 2: Neurology
    Version 8.125
    Latest signed off version: v8.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Amber
    • Literature
    Phenotypes
    • developmental and epileptic encephalopathy, MONDO:0100620
    Tags
    • Q3_25_promote_green
    • Q1_26_MOI
    Amber UNC13A in Intellectual disability


    Level 2: Developmental disorders
    Version 9.285
    Latest signed off version: v9.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Amber
    • Victorian Clinical Genetics Services
    • Literature
    Phenotypes
    • developmental and epileptic encephalopathy, MONDO:0100620
    Tags
    • Q3_25_promote_green
    • Q3_25_NHS_review
    • Q1_26_MOI