UNC79

unc-79 homolog, NALCN channel complex subunit
OMIM: 616884, Gene2Phenotype

3 panels

Panel Reviews Mode of inheritance Details
3 panels
Red UNC79 in DDG2P


Version 7.8
Latest signed off version: v7.0 (6 May 2026)

Component of the following Super Panels:

  • Paediatric disorders
  • review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • DD-Gene2Phenotype
    • Expert Review Red
    Phenotypes
    • UNC79-related intellectual disability with focal motor seizures
    Amber UNC79 in Early onset or syndromic epilepsy


    Level 2: Neurology
    Version 9.34
    Latest signed off version: v9.0 (6 May 2026)

    Component of the following Super Panels:

  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Amber
    • Literature
    Phenotypes
    • neurodevelopmental disorder, MONDO:0700092
    Tags
    • Q3_26_promote_green
    Amber UNC79 in Intellectual disability


    Level 2: Developmental disorders
    Version 10.54
    Latest signed off version: v10.0 (6 May 2026)

    Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
    Sources
    • Expert Review Amber
    • Literature
    Phenotypes
    • neurodevelopmental disorder, MONDO:0700092
    Tags
    • Q3_26_promote_green