Respiratory ciliopathies including non-CF bronchiectasis

Gene: CFAP43

Red List (low evidence)

CFAP43 (cilia and flagella associated protein 43)
EnsemblGeneIds (GRCh38): ENSG00000197748
EnsemblGeneIds (GRCh37): ENSG00000197748
OMIM: 617558, Gene2Phenotype
CFAP43 is in 3 panels

1 review

Achchuthan Shanmugasundram (Genomics England Curator)

Red List (low evidence)

The ClinGen Motile Ciliopathy expert panel has classified the association of autosomal recessive CFAP43 variants to primary ciliary dyskinesia (MONDO:0016575) as 'Disputed'. More information can be found in https://search.clinicalgenome.org/CCID:004425.
Sources: Literature
Created: 15 Jul 2025, 5:50 a.m.

Mode of inheritance
BIALLELIC, autosomal or pseudoautosomal

Phenotypes
Spermatogenic failure 19, OMIM:617592; primary ciliary dyskinesia, MONDO:0016575

Details

Mode of Inheritance
BIALLELIC, autosomal or pseudoautosomal
Sources
  • ClinGen
Phenotypes
  • Spermatogenic failure 19, OMIM:617592
  • primary ciliary dyskinesia, MONDO:0016575
Tags
disputed
OMIM
617558
Clinvar variants
Variants in CFAP43
Penetrance
None
Panels with this gene

History Filter Activity

17 Jul 2025, Gel status: 1

Added Tag

Achchuthan Shanmugasundram (Genomics England Curator)

Tag disputed tag was added to gene: CFAP43.

15 Jul 2025, Gel status: 1

Removed Source, Added New Source

Achchuthan Shanmugasundram (Genomics England Curator)

Source Literature was removed from CFAP43. Source ClinGen was added to CFAP43.

15 Jul 2025, Gel status: 1

Created, Added New Source, Set mode of inheritance, Set Phenotypes

Achchuthan Shanmugasundram (Genomics England Curator)

gene: CFAP43 was added gene: CFAP43 was added to Respiratory ciliopathies including non-CF bronchiectasis. Sources: Literature Mode of inheritance for gene: CFAP43 was set to BIALLELIC, autosomal or pseudoautosomal Phenotypes for gene: CFAP43 were set to Spermatogenic failure 19, OMIM:617592; primary ciliary dyskinesia, MONDO:0016575 Review for gene: CFAP43 was set to RED