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Hereditary neuropathy or pain disorder v6.148 ADA2 Sarah Leigh Tag Q3_24_promote_green was removed from gene: ADA2.
Tag Q3_24_NHS_review was removed from gene: ADA2.
Hereditary neuropathy or pain disorder v6.148 ADA2 Sarah Leigh edited their review of gene: ADA2: Added comment: The rating of this gene has been updated to green following NHS Genomic Medicine Service approval.; Changed mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Hereditary neuropathy or pain disorder v6.147 ADA2 Sarah Leigh Source NHS GMS was added to ADA2.
Source Expert Review Green was added to ADA2.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Hereditary neuropathy or pain disorder v5.40 ADA2 Sarah Leigh Tag Q3_24_promote_green tag was added to gene: ADA2.
Tag Q3_24_NHS_review tag was added to gene: ADA2.
Hereditary neuropathy or pain disorder v5.40 ADA2 Sarah Leigh reviewed gene: ADA2: Rating: GREEN; Mode of pathogenicity: None; Publications: ; Phenotypes: ; Mode of inheritance: None
Hereditary neuropathy or pain disorder v5.40 ADA2 Sarah Leigh Phenotypes for gene: ADA2 were changed from VASCULITIS; AUTOINFLAMMATION; IMMUNODEFICIENCY; HEMATOLOGIC DEFECTS; peripheral neuropathy; stroke to Vasculitis, autoinflammation, immunodeficiency, and hematologic defects syndrome, OMIM:615688; vasculitis due to ADA2 deficiency, MONDO:0014306
Hereditary neuropathy or pain disorder v5.39 ADA2 Sarah Leigh Classified gene: ADA2 as Amber List (moderate evidence)
Hereditary neuropathy or pain disorder v5.39 ADA2 Sarah Leigh Gene: ada2 has been classified as Amber List (Moderate Evidence).
Hereditary neuropathy or pain disorder v5.16 ADA2 Alexander Rossor gene: ADA2 was added
gene: ADA2 was added to Hereditary neuropathy or pain disorder. Sources: Expert list
Mode of inheritance for gene: ADA2 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: ADA2 were set to 34210540:37584090
Phenotypes for gene: ADA2 were set to VASCULITIS; AUTOINFLAMMATION; IMMUNODEFICIENCY; HEMATOLOGIC DEFECTS; peripheral neuropathy; stroke
Penetrance for gene: ADA2 were set to Complete
Review for gene: ADA2 was set to GREEN
Added comment: Sources: Expert list