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Hereditary neuropathy or pain disorder v6.163 ADPRHL2 Eleanor Williams commented on gene: ADPRHL2
Hereditary neuropathy or pain disorder v6.163 ADPRHL2 Eleanor Williams Tag new-gene-name tag was added to gene: ADPRHL2.
Hereditary neuropathy or pain disorder v6.148 ADPRHL2 Sarah Leigh Tag Q3_24_promote_green was removed from gene: ADPRHL2.
Tag Q3_24_NHS_review was removed from gene: ADPRHL2.
Hereditary neuropathy or pain disorder v6.148 ADPRHL2 Sarah Leigh edited their review of gene: ADPRHL2: Added comment: The rating of this gene has been updated to green following NHS Genomic Medicine Service approval.; Changed mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Hereditary neuropathy or pain disorder v6.147 ADPRHL2 Sarah Leigh Source NHS GMS was added to ADPRHL2.
Source Expert Review Green was added to ADPRHL2.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Hereditary neuropathy or pain disorder v5.50 ADPRHL2 Sarah Leigh Tag Q3_24_promote_green tag was added to gene: ADPRHL2.
Tag Q3_24_NHS_review tag was added to gene: ADPRHL2.
Hereditary neuropathy or pain disorder v5.50 ADPRHL2 Sarah Leigh reviewed gene: ADPRHL2: Rating: GREEN; Mode of pathogenicity: None; Publications: ; Phenotypes: ; Mode of inheritance: None
Hereditary neuropathy or pain disorder v5.50 ADPRHL2 Sarah Leigh Phenotypes for gene: ADPRHL2 were changed from Neurodegeneration; childhood-onset; ataxia; seizure; axonal polyneuropathy to Neurodegeneration, childhood-onset, stress-induced, with variable ataxia and seizures, OMIM:618170; neurodegeneration, childhood-onset, stress-induced, with variable ataxia and seizures, MONDO:0100095
Hereditary neuropathy or pain disorder v5.49 ADPRHL2 Sarah Leigh Publications for gene: ADPRHL2 were set to 30401461: 30100084
Hereditary neuropathy or pain disorder v5.48 ADPRHL2 Sarah Leigh Classified gene: ADPRHL2 as Amber List (moderate evidence)
Hereditary neuropathy or pain disorder v5.48 ADPRHL2 Sarah Leigh Gene: adprhl2 has been classified as Amber List (Moderate Evidence).
Hereditary neuropathy or pain disorder v5.16 ADPRHL2 Alexander Rossor gene: ADPRHL2 was added
gene: ADPRHL2 was added to Hereditary neuropathy or pain disorder. Sources: Expert list
Mode of inheritance for gene: ADPRHL2 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: ADPRHL2 were set to 30401461: 30100084
Phenotypes for gene: ADPRHL2 were set to Neurodegeneration; childhood-onset; ataxia; seizure; axonal polyneuropathy
Penetrance for gene: ADPRHL2 were set to Complete
Review for gene: ADPRHL2 was set to GREEN
Added comment: Sources: Expert list