Activity

Filter

Cancel
Date Panel Item Activity
9 actions
Hereditary neuropathy or pain disorder v6.148 AP5Z1 Sarah Leigh Tag Q3_24_promote_green was removed from gene: AP5Z1.
Tag Q3_24_NHS_review was removed from gene: AP5Z1.
Hereditary neuropathy or pain disorder v6.148 AP5Z1 Sarah Leigh commented on gene: AP5Z1: The rating of this gene has been updated to green following NHS Genomic Medicine Service approval.
Hereditary neuropathy or pain disorder v6.147 AP5Z1 Sarah Leigh Source NHS GMS was added to AP5Z1.
Source Expert Review Green was added to AP5Z1.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Hereditary neuropathy or pain disorder v6.26 AP5Z1 Sarah Leigh Tag Q3_24_promote_green tag was added to gene: AP5Z1.
Tag Q3_24_NHS_review tag was added to gene: AP5Z1.
Hereditary neuropathy or pain disorder v6.20 AP5Z1 Sarah Leigh reviewed gene: AP5Z1: Rating: GREEN; Mode of pathogenicity: ; Publications: 20613862: 24833714; Phenotypes: Spastic paraplegia 48, autosomal recessive, OMIM:613647; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Hereditary neuropathy or pain disorder v5.64 AP5Z1 Sarah Leigh Phenotypes for gene: AP5Z1 were changed from spasticity; ataxia; retinopathy; neuropathy; parkinsonism to Spastic paraplegia 48, autosomal recessive, OMIM:613647; hereditary spastic paraplegia 48, MONDO:0013342
Hereditary neuropathy or pain disorder v5.63 AP5Z1 Sarah Leigh Classified gene: AP5Z1 as Amber List (moderate evidence)
Hereditary neuropathy or pain disorder v5.63 AP5Z1 Sarah Leigh Gene: ap5z1 has been classified as Amber List (Moderate Evidence).
Hereditary neuropathy or pain disorder v5.19 AP5Z1 Alexander Rossor gene: AP5Z1 was added
gene: AP5Z1 was added to Hereditary neuropathy or pain disorder. Sources: Expert list
Mode of inheritance for gene: AP5Z1 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: AP5Z1 were set to 26085577
Phenotypes for gene: AP5Z1 were set to spasticity; ataxia; retinopathy; neuropathy; parkinsonism
Penetrance for gene: AP5Z1 were set to Complete
Review for gene: AP5Z1 was set to AMBER
Added comment: only a single patient with neuropathy
Sources: Expert list