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Osteogenesis imperfecta v1.49 B4GALT7 Eleanor Williams Classified gene: B4GALT7 as Green List (high evidence)
Osteogenesis imperfecta v1.49 B4GALT7 Eleanor Williams Added comment: Comment on list classification: This gene was discussed in the GMS musculoskeletal specialist test group Webex on 2019-06-04. It was decided that due to further evidence, it should be made green.
Osteogenesis imperfecta v1.49 B4GALT7 Eleanor Williams Gene: b4galt7 has been classified as Green List (High Evidence).
Osteogenesis imperfecta v1.38 B4GALT7 Eleanor Williams Mode of inheritance for gene: B4GALT7 was changed from to BIALLELIC, autosomal or pseudoautosomal
Osteogenesis imperfecta v1.36 B4GALT7 Eleanor Williams commented on gene: B4GALT7: This gene was discussed in the GMS musculoskeletal specialist test group Webex on 2019-06-04. It was decided that due to further evidence, it should be made green.
Osteogenesis imperfecta v1.36 B4GALT7 Eleanor Williams Publications for gene: B4GALT7 were set to 15211654; 26940150
Osteogenesis imperfecta v1.35 B4GALT7 Eleanor Williams commented on gene: B4GALT7: Associated with Ehlers-Danlos syndrome, spondylodysplastic type, 1 (#130070) in OMIM.

PMID: 26940150 - Salter et al 2016 - two unrelated patients with compound heterozygous mutations in B4GALT7. Both showed osteopenia (one with fractures, other patient had mild osteopenia). They review the phenotypes reported in previous cases (Table 1): 1 case with osteopenia reported in Faiyaz‐Ul‐Haque et al. [2004] , 1 case reported in Kresse et al. [1987] (with possible rib fracture).

Summary: 3 cases of patients with homozygous or compound heterozygous variants in B4GALT7 and osteopenia, two with fractures.
Osteogenesis imperfecta v1.23 B4GALT7 Eleanor Williams Publications for gene: B4GALT7 were set to
Osteogenesis imperfecta v1.22 B4GALT7 Eleanor Williams Phenotypes for gene: B4GALT7 were changed from Osteogenesis Imperfecta and Decreased Bone Density; skeletal dysplasias to Osteogenesis Imperfecta and Decreased Bone Density; skeletal dysplasias; Ehlers-Danlos syndrome, spondylodysplastic type, 1 130070
Osteogenesis imperfecta v1.19 B4GALT7 Duncan Baker reviewed gene: B4GALT7: Rating: GREEN; Mode of pathogenicity: ; Publications: 26940150; Phenotypes: Ehlers-Danlos syndrome, spondylodysplastic type, 1 130070; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Osteogenesis imperfecta v1.18 B4GALT7 Eleanor Williams reviewed gene: B4GALT7: Rating: AMBER; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance:
Osteogenesis imperfecta v1.17 B4GALT7 Eleanor Williams Source NHS GMS was added to B4GALT7.