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Intellectual disability v9.387 CACNA1D Ida Ertmanska changed review comment from: Comment on mode of inheritance: Individuals reported with biallelic CACNA1D variants present with deafness and sinoatrial node dysfunction - no epilepsy or cognitive impairment (PMIDs: 21131953; 30498240; 30054272; 32747562). Monoallelic de novo variants result in primary aldosteronism, seizures, and neurologic abnormalities (more than 3 unrelated cases e.g., PMIDs: 23913001, 2847230; 37122292). The literature review by Alzahrani et al., 2023 (PMID: 37122292) states that intellectual disability affects 80% of patients, and seizures are present in 47% of cases of the dominant disorder. Hence, the mode of inheritance on Early onset or syndromic epilepsy should be changed to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted at the next update.; to: Comment on mode of inheritance: Individuals reported with biallelic CACNA1D variants present with deafness and sinoatrial node dysfunction - no epilepsy or cognitive impairment (PMIDs: 21131953; 30498240; 30054272; 32747562). Monoallelic de novo variants result in primary aldosteronism, seizures, and neurologic abnormalities (more than 3 unrelated cases e.g., PMIDs: 23913001, 2847230; 37122292). The literature review by Alzahrani et al., 2023 (PMID: 37122292) states that intellectual disability affects 80% of patients, and seizures are present in 47% of cases of the dominant disorder. Hence, the mode of inheritance on Intellectual disability should be changed to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted at the next update.
Intellectual disability v9.382 CACNA1D Ida Ertmanska Phenotypes for gene: CACNA1D were changed from Primary aldosteronism, seizures, and neurologic abnormalities 615474 AD; Sinoatrial node dysfunction and deafness 614896 AR to Primary aldosteronism, seizures, and neurologic abnormalities, OMIM:615474; aldosterone-producing adenoma with seizures and neurological abnormalities, MONDO:0014200
Intellectual disability v9.381 CACNA1D Ida Ertmanska Publications for gene: CACNA1D were set to 28472301; 23913001
Intellectual disability v9.380 CACNA1D Ida Ertmanska Tag Q2_26_MOI tag was added to gene: CACNA1D.
Intellectual disability v9.380 CACNA1D Ida Ertmanska reviewed gene: CACNA1D: Rating: GREEN; Mode of pathogenicity: None; Publications: 21131953, 30498240, 30054272, 32747562, 23913001, 2847230, 37122292; Phenotypes: Primary aldosteronism, seizures, and neurologic abnormalities, OMIM:615474, aldosterone-producing adenoma with seizures and neurological abnormalities, MONDO:0014200; Mode of inheritance: MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Intellectual disability v3.797 CACNA1D Ivone Leong Source: Expert Review Red was removed from gene: CACNA1D