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Cleidocranial Dysplasia v1.6 CBFB Arina Puzriakova Tag Q2_24_promote_green was removed from gene: CBFB.
Tag Q2_24_MOI was removed from gene: CBFB.
Tag Q2_24_NHS_review was removed from gene: CBFB.
Cleidocranial Dysplasia v1.6 CBFB Arina Puzriakova reviewed gene: CBFB: Rating: GREEN; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance: MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Cleidocranial Dysplasia v1.5 CBFB Arina Puzriakova Source Expert Review Green was added to CBFB.
Source NHS GMS was added to CBFB.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Cleidocranial Dysplasia v1.4 CBFB Sarah Leigh Phenotypes for gene: CBFB were changed from cleidocranial dysplasia; dental anomalies such as supernumery teeth and eruption failure; developmental delay (variable); shortening of the distal phalanges to Cleidocranial dysplasia 2, OMIM:620099; cleidocranial dysplasia 2, MONDO:0859307
Cleidocranial Dysplasia v1.3 CBFB Sarah Leigh Publications for gene: CBFB were set to PMID: 36241386
Cleidocranial Dysplasia v1.2 CBFB Sarah Leigh Tag Q2_24_promote_green tag was added to gene: CBFB.
Tag Q2_24_MOI tag was added to gene: CBFB.
Tag Q2_24_NHS_review tag was added to gene: CBFB.
Cleidocranial Dysplasia v1.2 CBFB Sarah Leigh Classified gene: CBFB as Amber List (moderate evidence)
Cleidocranial Dysplasia v1.2 CBFB Sarah Leigh Gene: cbfb has been classified as Amber List (Moderate Evidence).
Cleidocranial Dysplasia v1.1 CBFB Sarah Leigh reviewed gene: CBFB: Rating: GREEN; Mode of pathogenicity: None; Publications: ; Phenotypes: ; Mode of inheritance: None
Cleidocranial Dysplasia v1.1 CBFB Alistair Pagnamenta gene: CBFB was added
gene: CBFB was added to Cleidocranial Dysplasia. Sources: Literature
Mode of inheritance for gene: CBFB was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: CBFB were set to PMID: 36241386
Phenotypes for gene: CBFB were set to cleidocranial dysplasia; dental anomalies such as supernumery teeth and eruption failure; developmental delay (variable); shortening of the distal phalanges
Penetrance for gene: CBFB were set to Complete
Review for gene: CBFB was set to GREEN
gene: CBFB was marked as current diagnostic
Added comment: Beyltjens et al describe 8 individuals from 5 families (ascertained via GeneMatcher) with cleidocranial dysplasia and rare severe consequence variants in CBFB. Previous analysis of RUNX2 had been negative. CBFB encodes the core-binding factor β subunit, which can interact with RUNX2 to form a heterodimeric transcription factor - so biologically was a good candidate gene, even before the Beyltjens et al study. Aware of data in 100kGP that supports this new gene-disease association.
Sources: Literature