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Retinal disorders v7.8 DCT Achchuthan Shanmugasundram Tag Q3_24_promote_green was removed from gene: DCT.
Tag Q3_24_NHS_review was removed from gene: DCT.
Retinal disorders v7.8 DCT Achchuthan Shanmugasundram reviewed gene: DCT: Rating: GREEN; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Retinal disorders v7.7 DCT Achchuthan Shanmugasundram Source NHS GMS was added to DCT.
Source Expert Review Green was added to DCT.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Retinal disorders v7.1 DCT Achchuthan Shanmugasundram Tag Q3_24_MOI was removed from gene: DCT.
Retinal disorders v6.15 DCT Sarah Leigh Tag Q3_24_promote_green tag was added to gene: DCT.
Tag Q3_24_NHS_review tag was added to gene: DCT.
Tag Q3_24_MOI tag was added to gene: DCT.
Retinal disorders v6.15 DCT Sarah Leigh reviewed gene: DCT: Rating: GREEN; Mode of pathogenicity: None; Publications: ; Phenotypes: ; Mode of inheritance: None
Retinal disorders v6.15 DCT Sarah Leigh Phenotypes for gene: DCT were changed from oculocutaneous albinism; foveal hypoplasia; chiasmal misrouting; iris transillumination defect; nystagmus; ocular hypopigmentation to Oculocutaneous albinism, type VIII, OMIM:619165; oculocutaneous albinism type 8, MONDO:0030899
Retinal disorders v6.14 DCT Sarah Leigh Publications for gene: DCT were set to (Pennamen et al., 2021) (PMID: 33100333); (Volk et al., 2021) (PMID: 33959807)
Retinal disorders v6.13 DCT Sarah Leigh Classified gene: DCT as Amber List (moderate evidence)
Retinal disorders v6.13 DCT Sarah Leigh Gene: dct has been classified as Amber List (Moderate Evidence).
Retinal disorders v5.15 DCT Mohammed Derar gene: DCT was added
gene: DCT was added to Retinal disorders. Sources: Literature
Mode of inheritance for gene: DCT was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: DCT were set to (Pennamen et al., 2021) (PMID: 33100333); (Volk et al., 2021) (PMID: 33959807)
Phenotypes for gene: DCT were set to oculocutaneous albinism; foveal hypoplasia; chiasmal misrouting; iris transillumination defect; nystagmus; ocular hypopigmentation
Penetrance for gene: DCT were set to Complete
Review for gene: DCT was set to GREEN
Added comment: Biallelic variants in DCT are reported to cause oculocutaneous albinism type 8 in multiple unrelated and affected families. This form of albinism has subtle hypopigmentation and displays the classical ocular manifestations of foveal hypoplasia, iris transillumination defect and fundus hypopigmentation. It is therefore imperative to sprobe DCT in patients with retinal abnormalities and presumbly normal pigmentation.
Sources: Literature