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Fetal hydrops v1.100 DOK7 Arina Puzriakova Classified gene: DOK7 as Amber List (moderate evidence)
Fetal hydrops v1.100 DOK7 Arina Puzriakova Gene: dok7 has been classified as Amber List (Moderate Evidence).
Fetal hydrops v1.16 DOK7 Zornitza Stark gene: DOK7 was added
gene: DOK7 was added to Fetal hydrops. Sources: Expert list
Mode of inheritance for gene: DOK7 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: DOK7 were set to 31880392; 19261599
Phenotypes for gene: DOK7 were set to Fetal akinesia sequence, MIM#618389
Review for gene: DOK7 was set to AMBER
gene: DOK7 was marked as current diagnostic
Added comment: Two unrelated families reported with fetal akinesia deformation sequence, hydrops is a feature. The gene also causes a less severe phenotype (congenital myasthenic syndrome 10), hydrops is not a feature of this.
Sources: Expert list