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Amelogenesis imperfecta v4.33 DSPP Ida Ertmanska changed review comment from: PMID: 39806231 Gilani, Saikia, and Anthonappa, 2025
Lit review of 322 cases with non-syndromic dentinogenesis imperfecta (DI - characterized clinically by amber or gray-yellow opalescent tooth discoloration, obliteration of pulp chambers and root canals, and attrition. Both deciduous and permanent teeth are affected (PMID: 18456718 Song et al., 2008).
DSPP mutations were the most frequent, with with 59 documented variants from 37 publications. 34/59 variants were in exon 5 of DSPP.
Sources: Literature; to: PMID: 39806231 Gilani, Saikia, and Anthonappa, 2025
Lit review of 322 cases with non-syndromic dentinogenesis imperfecta (DI - characterized clinically by amber or gray-yellow opalescent tooth discoloration, obliteration of pulp chambers and root canals, and attrition. Both deciduous and permanent teeth are affected (PMID: 18456718 Song et al., 2008)).
DSPP mutations were the most frequent, with 59 documented variants from 37 publications. 34/59 variants were in exon 5 of DSPP.
Sources: Literature
Amelogenesis imperfecta v4.33 DSPP Ida Ertmanska edited their review of gene: DSPP: Changed publications to: 18456718, 39806231
Amelogenesis imperfecta v4.33 DSPP Ida Ertmanska Classified gene: DSPP as Amber List (moderate evidence)
Amelogenesis imperfecta v4.33 DSPP Ida Ertmanska Gene: dspp has been classified as Amber List (Moderate Evidence).
Amelogenesis imperfecta v4.32 DSPP Ida Ertmanska Publications for gene: DSPP were set to 1845671839806231
Amelogenesis imperfecta v4.31 DSPP Ida Ertmanska gene: DSPP was added
gene: DSPP was added to Amelogenesis imperfecta. Sources: Literature
Mode of inheritance for gene: DSPP was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Publications for gene: DSPP were set to 1845671839806231
Phenotypes for gene: DSPP were set to Deafness, autosomal dominant 39, with dentinogenesis, OMIM:605594; Dentin dysplasia, type II, OMIM:125420; Dentinogenesis imperfecta, Shields type II, OMIM:125490; Dentinogenesis imperfecta, Shields type III, OMIM:125500
Review for gene: DSPP was set to GREEN
Added comment: PMID: 39806231 Gilani, Saikia, and Anthonappa, 2025
Lit review of 322 cases with non-syndromic dentinogenesis imperfecta (DI - characterized clinically by amber or gray-yellow opalescent tooth discoloration, obliteration of pulp chambers and root canals, and attrition. Both deciduous and permanent teeth are affected (PMID: 18456718 Song et al., 2008).
DSPP mutations were the most frequent, with with 59 documented variants from 37 publications. 34/59 variants were in exon 5 of DSPP.
Sources: Literature