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Early onset or syndromic epilepsy v8.138 ELFN1 Arina Puzriakova Tag Q3_25_promote_green was removed from gene: ELFN1.
Early onset or syndromic epilepsy v8.134 ELFN1 Achchuthan Shanmugasundram reviewed gene: ELFN1: Rating: GREEN; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance:
Early onset or syndromic epilepsy v8.134 ELFN1 Arina Puzriakova Source NHS GMS was added to ELFN1.
Source Expert Review Green was added to ELFN1.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Early onset or syndromic epilepsy v8.25 ELFN1 Arina Puzriakova Classified gene: ELFN1 as Amber List (moderate evidence)
Early onset or syndromic epilepsy v8.25 ELFN1 Arina Puzriakova Added comment: Comment on list classification: There is sufficient evidence to promote this gene to Green at the next GMS panel update.
Early onset or syndromic epilepsy v8.25 ELFN1 Arina Puzriakova Gene: elfn1 has been classified as Amber List (Moderate Evidence).
Early onset or syndromic epilepsy v8.24 ELFN1 Arina Puzriakova gene: ELFN1 was added
gene: ELFN1 was added to Early onset or syndromic epilepsy. Sources: Literature
Q3_25_promote_green tags were added to gene: ELFN1.
Mode of inheritance for gene: ELFN1 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: ELFN1 were set to 40576023; 34509675; 34452636
Phenotypes for gene: ELFN1 were set to Neurodevelopmental disorder, MONDO:0700092
Review for gene: ELFN1 was set to GREEN
Added comment: Total of 14 individuals from 7 unrelated families with biallelic loss of function variants in ELFN1 and a neurodevelopmental disorder comprising DD/ID ranging from moderate to severe (13/13) and epilepsy (12/13). Other features included dysmorphic features, behavioural disturbances, ADHD, ASD, hypotonia, muscle weakness, ataxia. Knockout and haploinsufficiency studies in mice resulted in detectable phenotypes compatible with ELFN1 deficiency disorder.
Sources: Literature