Activity
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28 actions
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| Hereditary ataxia with onset in adulthood v8.30 | GDAP2 | Ida Ertmanska Tag gene-checked was removed from gene: GDAP2. | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v8.30 | GDAP2 | Ida Ertmanska Tag gene-checked tag was added to gene: GDAP2. | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v8.26 | GDAP2 |
Arina Puzriakova Tag Q4_24_NHS_review was removed from gene: GDAP2. Tag Q4_24_promote_green was removed from gene: GDAP2. |
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| Hereditary ataxia with onset in adulthood v8.25 | GDAP2 | Achchuthan Shanmugasundram reviewed gene: GDAP2: Rating: GREEN; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance: | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v8.24 | GDAP2 |
Arina Puzriakova Source Expert Review Green was added to GDAP2. Rating Changed from Amber List (moderate evidence) to Green List (high evidence) |
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| Hereditary ataxia with onset in adulthood v7.6 | GDAP2 |
Sarah Leigh Tag Q4_24_NHS_review tag was added to gene: GDAP2. Tag Q4_24_promote_green tag was added to gene: GDAP2. |
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| Hereditary ataxia with onset in adulthood v7.6 | GDAP2 |
Sarah Leigh changed review comment from: Biallelic GDAP2 variants have been associated with Spinocerebellar ataxia, autosomal recessive 27 (OMIM:618369), but this gene has not been associated with a phenotype in G2P. At least seven variants have been reported in at least six unrelated cases of OMIM:618369 (PMID: 30084953;32437512;32428220;37070050;38587696).; to: Biallelic GDAP2 variants have been associated with Spinocerebellar ataxia, autosomal recessive 27 (OMIM:618369), but this gene has not been associated with a phenotype in G2P. At least seven variants have been reported in at least six unrelated cases of OMIM:618369 (PMID: 30084953;32437512;32428220;37070050;38587696). The Gdap2 knockdown of Drosophila model resulted in shortened lifespan and motor anomalies that resembled the human phenotype (PMID: 30084953). In vitro expression levels of variants: p.Gln316*, p.His400fs*15 and p.Ser436fs*3 transcripts were reduced in comparison to wild type, resulting in barely detectable levels of variant protein. The transcripts of the remaining variants (p.Thr442fs*7 and p.Arg253*) tested resulted in truncated proteins (PMID: 32437512). |
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| Hereditary ataxia with onset in adulthood v7.6 | GDAP2 | Sarah Leigh reviewed gene: GDAP2: Rating: GREEN; Mode of pathogenicity: None; Publications: ; Phenotypes: ; Mode of inheritance: None | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v7.6 | GDAP2 | Sarah Leigh Phenotypes for gene: GDAP2 were changed from Autosomal recessive spinocerebellar ataxia to Spinocerebellar ataxia, autosomal recessive 27, OMIM:618369; spinocerebellar ataxia, autosomal recessive 27, MONDO:0032706 | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v7.5 | GDAP2 | Sarah Leigh Publications for gene: GDAP2 were set to 30084953; 32437512; 32428220; 37070050 | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v7.4 | GDAP2 | Sarah Leigh Publications for gene: GDAP2 were set to 30084953; 32437512 | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v7.3 | GDAP2 | Sarah Leigh Publications for gene: GDAP2 were set to | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.188 | GDAP2 | Louise Daugherty commented on gene: GDAP2: Downgraded rating from Green to Amber. As discussed with the GMS Neurology Specialist Test Group webex call 26th July 2019: The Specialist Test Group all agreed that there is only enough evidence to rate this gene Amber | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.187 | GDAP2 |
Louise Daugherty Source Expert Review Amber was added to GDAP2. Rating Changed from Green List (high evidence) to Amber List (moderate evidence) |
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| Hereditary ataxia with onset in adulthood v1.20 | GDAP2 | Louise Daugherty Phenotypes for gene: GDAP2 were changed from Autosomal recessive spinocerebellar ataxia, not listed in to Autosomal recessive spinocerebellar ataxia | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.19 | GDAP2 | Louise Daugherty Mode of inheritance for gene: GDAP2 was changed from to BIALLELIC, autosomal or pseudoautosomal | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.18 | GDAP2 | Louise Daugherty Classified gene: GDAP2 as Green List (high evidence) | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.18 | GDAP2 | Louise Daugherty Gene: gdap2 has been classified as Green List (High Evidence). | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.17 | GDAP2 | Louise Daugherty Classified gene: GDAP2 as Green List (high evidence) | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.17 | GDAP2 | Louise Daugherty Gene: gdap2 has been classified as Green List (High Evidence). | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.14 | GDAP2 | Louise Daugherty commented on gene: GDAP2: Review and rating submitted byJames Polke (North Bristol NHS Trust), on behalf of London North GLH for GMS Neurology specialist test group | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.13 | GDAP2 | Louise Daugherty Source London North GMS was added to GDAP2. | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.11 | GDAP2 | James Polke reviewed gene: GDAP2: Rating: RED; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance: | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.9 | GDAP2 | Louise Daugherty Added phenotypes Autosomal recessive spinocerebellar ataxia, not listed in for gene: GDAP2 | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.8 | GDAP2 | Louise Daugherty reviewed gene: GDAP2: Rating: AMBER; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance: | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.7 | GDAP2 | Tracy Lester reviewed gene: GDAP2: Rating: GREEN; Mode of pathogenicity: ; Publications: ; Phenotypes: Autosomal recessive spinocerebellar ataxia, not listed in ; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.2 | GDAP2 | Louise Daugherty Source NHS GMS was added to GDAP2. | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Hereditary ataxia with onset in adulthood v1.1 | GDAP2 |
Louise Daugherty gene: GDAP2 was added gene: GDAP2 was added to Hereditary ataxia - adult onset. Sources: Wessex and West Midlands GLH Mode of inheritance for gene: GDAP2 was set to |
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