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Renal ciliopathies v1.52 IFT172 Eleanor Williams Phenotypes for gene: IFT172 were changed from Short-rib thoracic dysplasia 10 with or without polydactyly, MIM# 615630 to Short-rib thoracic dysplasia 10 with or without polydactyly, OMIM:615630
Renal ciliopathies v1.51 IFT172 Eleanor Williams Tag for-review was removed from gene: IFT172.
Renal ciliopathies v1.51 IFT172 Eleanor Williams commented on gene: IFT172
Renal ciliopathies v1.50 IFT172 Eleanor Williams Source Expert Review Green was added to IFT172.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Renal ciliopathies v1.30 IFT172 Arina Puzriakova Classified gene: IFT172 as Amber List (moderate evidence)
Renal ciliopathies v1.30 IFT172 Arina Puzriakova Added comment: Comment on list classification: Changed rating to Amber so that Green genes on this panel reflect the NHS signed-off version. This will be reviewed at the next GMS panel update.
Renal ciliopathies v1.30 IFT172 Arina Puzriakova Gene: ift172 has been classified as Amber List (Moderate Evidence).
Renal ciliopathies v1.16 IFT172 Eleanor Williams Tag for-review tag was added to gene: IFT172.
Renal ciliopathies v1.9 IFT172 Catherine Snow Classified gene: IFT172 as Green List (high evidence)
Renal ciliopathies v1.9 IFT172 Catherine Snow Added comment: Comment on list classification: A number of publications identify relationship of variants in IFT172 and phenotypes associated with Bardet-Biedl syndrome and Jeune and Mainzer-Saldino Syndromes, all are ciliopathy diseases. The range of phenotypes can result in serve skeletal and multiple affected organs but also includes a reported case of non-syndromic retinal dystrophy.
Sufficient numbers of unrelated individuals reported to have kidney dysfunction to include IFT172 as Green on the panel.
Renal ciliopathies v1.9 IFT172 Catherine Snow Gene: ift172 has been classified as Green List (High Evidence).
Renal ciliopathies v1.8 IFT172 Catherine Snow Publications for gene: IFT172 were set to
Renal ciliopathies v1.0 IFT172 Zornitza Stark gene: IFT172 was added
gene: IFT172 was added to Renal ciliopathies. Sources: Expert list
Mode of inheritance for gene: IFT172 was set to BIALLELIC, autosomal or pseudoautosomal
Phenotypes for gene: IFT172 were set to Short-rib thoracic dysplasia 10 with or without polydactyly, MIM# 615630
Review for gene: IFT172 was set to GREEN
Added comment: Nephronophthisis is a recognised feature of this ciliopathy.
Sources: Expert list