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Cerebral vascular malformations v4.7 ITGB1 Ida Ertmanska edited their review of gene: ITGB1: Changed mode of inheritance: Unknown
Cerebral vascular malformations v4.7 ITGB1 Ida Ertmanska edited their review of gene: ITGB1: Added comment: Comment on list classification: There are two patients reported in literature with Vein of Galen aneurysmal malformation and LoF variants in ITGB1 (presumed monoallelic but not specified). This gene should be rated Amber for Cerebral vascular malformations until more evidence is reported.; Changed mode of inheritance: MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Cerebral vascular malformations v4.7 ITGB1 Ida Ertmanska Phenotypes for gene: ITGB1 were changed from Vein of Galen Malformation to Vein of Galen aneurysmal malformation, HP:0030713
Cerebral vascular malformations v4.6 ITGB1 Ida Ertmanska Classified gene: ITGB1 as Amber List (moderate evidence)
Cerebral vascular malformations v4.6 ITGB1 Ida Ertmanska Gene: itgb1 has been classified as Amber List (Moderate Evidence).
Cerebral vascular malformations v4.5 ITGB1 Ida Ertmanska reviewed gene: ITGB1: Rating: AMBER; Mode of pathogenicity: None; Publications: 37978175; Phenotypes: Vein of Galen aneurysmal malformation, HP:0030713; Mode of inheritance: None
Cerebral vascular malformations v3.26 ITGB1 Alexandra Njegic gene: ITGB1 was added
gene: ITGB1 was added to Cerebral vascular malformations. Sources: Literature
Mode of inheritance for gene: ITGB1 was set to MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Publications for gene: ITGB1 were set to 37978175
Phenotypes for gene: ITGB1 were set to Vein of Galen Malformation
Penetrance for gene: ITGB1 were set to Incomplete
Review for gene: ITGB1 was set to AMBER
Added comment: 37978175 (including PMID 30578106 cohort): combined 2 probands, 1 unphased frameshift and 1 transmitted splice variant, in silico modelling predicted NMD, pathogenicity given as 'likely damaging'.
Sources: Literature