Activity

Filter

Cancel
Date Panel Item Activity
10 actions
Retinal disorders v8.88 MDM1 Arina Puzriakova Tag Q1_26_NHS_review tag was added to gene: MDM1.
Retinal disorders v8.88 MDM1 Arina Puzriakova Classified gene: MDM1 as Amber List (moderate evidence)
Retinal disorders v8.88 MDM1 Arina Puzriakova Added comment: Comment on list classification: There is sufficient evidence to promote this gene to Green at the next GMS panel update - 5 unrelated cases with retinal dystrophy due to biallelic variants in this gene. Localisation in cilia indicate that MDM1 variants are associated with a first-order ciliopathy.
Retinal disorders v8.88 MDM1 Arina Puzriakova Gene: mdm1 has been classified as Amber List (Moderate Evidence).
Retinal disorders v8.87 MDM1 Arina Puzriakova Tag Q1_26_promote_green tag was added to gene: MDM1.
Retinal disorders v8.87 MDM1 Arina Puzriakova Phenotypes for gene: MDM1 were changed from Retinal dystrophy to Retinal dystrophy, HP:0000556
Publications for gene: MDM1 were updated from PMID: 41742423 to 41742423
Retinal disorders v8.86 MDM1 Arina Puzriakova edited their review of gene: MDM1: Added comment: PMID: 41742423 (2026) - 6 individuals from 5 unrelated families with biallelic predicted null variants in MDM1 (aka SAXO6). Ophthalmic examination revealed retinitis pigmentosa in 4 individuals and cone-rod dystrophy in 2 individuals.
SAXO6 was shown to co-localise with distinct ciliary microtubules from the immotile cilium present in rod and cone photoreceptors in human retina, and mass spectrometry demonstrated an interaction with α-tubulin, supporting its classification as a microtubule inner protein.

This gene is not yet associated with any phenotype in OMIM or G2P.; Changed rating: GREEN; Changed publications to: 41742423; Changed phenotypes to: Retinal dystrophy, HP:0000556; Changed mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Retinal disorders v8.86 MDM1 Arina Puzriakova commented on gene: MDM1
Retinal disorders v8.86 MDM1 Arina Puzriakova Tag new-gene-name tag was added to gene: MDM1.
Retinal disorders v8.86 MDM1 Siying Lin gene: MDM1 was added
gene: MDM1 was added to Retinal disorders. Sources: Literature
Mode of inheritance for gene: MDM1 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: MDM1 were set to PMID: 41742423
Phenotypes for gene: MDM1 were set to Retinal dystrophy
Penetrance for gene: MDM1 were set to unknown
Mode of pathogenicity for gene: MDM1 was set to Other
Review for gene: MDM1 was set to GREEN
Added comment: Recent publication (PMID: 41742423) reporting 6 affected individuals from 5 families with biallelic loss of function variants in MDM1 (also known as SAXO6) and retinal dystrophy
Sources: Literature