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Intellectual disability v9.57 MED16 Achchuthan Shanmugasundram Classified gene: MED16 as Amber List (moderate evidence)
Intellectual disability v9.57 MED16 Achchuthan Shanmugasundram Added comment: Comment on list classification: There is sufficient evidence (10 unrelated families) available for the promotion of this gene to green rating in the next GMS update.
Intellectual disability v9.57 MED16 Achchuthan Shanmugasundram Gene: med16 has been classified as Amber List (Moderate Evidence).
Intellectual disability v9.56 MED16 Achchuthan Shanmugasundram Tag Q3_25_promote_green tag was added to gene: MED16.
Tag Q3_25_NHS_review tag was added to gene: MED16.
Intellectual disability v9.56 MED16 Achchuthan Shanmugasundram Phenotypes for gene: MED16 were changed from developmental delay; multiple congenital abnormalities; Medopathy to Guillouet-Gordon syndrome, OMIM:621220
Intellectual disability v9.56 MED16 Achchuthan Shanmugasundram Publications for gene: MED16 were set to PMID: 40081376
Intellectual disability v9.55 MED16 Achchuthan Shanmugasundram reviewed gene: MED16: Rating: GREEN; Mode of pathogenicity: None; Publications: 40081376; Phenotypes: Guillouet-Gordon syndrome, OMIM:621220; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Intellectual disability v9.51 MED16 Karen Stals gene: MED16 was added
gene: MED16 was added to Intellectual disability. Sources: NHS GMS
Mode of inheritance for gene: MED16 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: MED16 were set to PMID: 40081376
Phenotypes for gene: MED16 were set to developmental delay; multiple congenital abnormalities; Medopathy
Penetrance for gene: MED16 were set to unknown
Review for gene: MED16 was set to GREEN
gene: MED16 was marked as current diagnostic
Added comment: 25 individuals from 18 families reported with biallelic MED16 variants with multiple congenital anomalies (MCAs)-intellectual disability syndrome. Intellectual disability, speech delay, and/or motor delay of variable severity were constant and associated with variable combinations of craniofacial defects (micro/retrognathia, cleft palate, and preauricular tags), anomalies of the extremities, and heart defects (predominantly tetralogy of Fallot). Visual impairment, deafness, and magnetic resonance imaging (MRI) abnormalities were also frequent. 8 predicted protein-truncating and 18 missense or in-frame duplication variants identified.
Sources: NHS GMS