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Multiple monogenic benign skin tumours v1.11 MSH6 Ivone Leong Phenotypes for gene: MSH6 were changed from Muir-Torre syndrome to Muir-Torre syndrome, MONDO:0008018
Multiple monogenic benign skin tumours v0.11 MSH6 Catherine Snow Classified gene: MSH6 as Amber List (moderate evidence)
Multiple monogenic benign skin tumours v0.11 MSH6 Catherine Snow Gene: msh6 has been classified as Amber List (Moderate Evidence).
Multiple monogenic benign skin tumours v0.8 MSH6 Anna de Burca gene: MSH6 was added
gene: MSH6 was added to Multiple monogenic benign skin tumours. Sources: Expert list
Mode of inheritance for gene: MSH6 was set to MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Phenotypes for gene: MSH6 were set to Muir-Torre syndrome
Review for gene: MSH6 was set to AMBER
Added comment: There have been rare reports of MSH6 causing a Muir-Torre phenotype.
Sources: Expert list