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Hereditary neuropathy or pain disorder v6.148 NFASC Sarah Leigh Tag Q3_24_promote_green was removed from gene: NFASC.
Tag Q3_24_NHS_review was removed from gene: NFASC.
Hereditary neuropathy or pain disorder v6.148 NFASC Sarah Leigh reviewed gene: NFASC: Rating: GREEN; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Hereditary neuropathy or pain disorder v6.147 NFASC Sarah Leigh Source NHS GMS was added to NFASC.
Source Expert Review Green was added to NFASC.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Hereditary neuropathy or pain disorder v6.55 NFASC Achchuthan Shanmugasundram Classified gene: NFASC as Amber List (moderate evidence)
Hereditary neuropathy or pain disorder v6.55 NFASC Achchuthan Shanmugasundram Added comment: Comment on list classification: There are at least three unrelated cases with syndromic neuropathy. Hence, this gene can be recommended for promotion to green rating in the next GMS update.
Hereditary neuropathy or pain disorder v6.55 NFASC Achchuthan Shanmugasundram Gene: nfasc has been classified as Amber List (Moderate Evidence).
Hereditary neuropathy or pain disorder v6.54 NFASC Achchuthan Shanmugasundram Phenotypes for gene: NFASC were changed from Developmental delay; peripheral neuropathy to Neurodevelopmental disorder with central and peripheral motor dysfunction, OMIM:618356
Hereditary neuropathy or pain disorder v6.53 NFASC Achchuthan Shanmugasundram Publications for gene: NFASC were set to 30850329: 30124836
Hereditary neuropathy or pain disorder v6.52 NFASC Achchuthan Shanmugasundram Tag Q3_24_promote_green tag was added to gene: NFASC.
Tag Q3_24_NHS_review tag was added to gene: NFASC.
Hereditary neuropathy or pain disorder v6.52 NFASC Achchuthan Shanmugasundram commented on gene: NFASC: PMID:30850329 reported the identification of a homozygous NFASC variant (p.Val1122Glu) in two siblings from an Italian family. The patients presented with early-onset cerebellar ataxia and demyelinating neuropathy.

PMID:31501903 reported the identification of one frameshift and four different homozygous non-synonymous variants in NFASC gene in ten individuals from six unrelated families. They presented with a neurodevelopmental disorder characterised with a spectrum of central (intellectual disability, developmental delay, motor impairment, speech difficulties) and peripheral (early onset demyelinating neuropathy) neurological involvement. Neuropathy was reported in at least three patients from two different families.

This gene has been associated with relevant phenotype in OMIM (MIM #618356), which lists demyelinating sensorimotor polyneuropathy as one of the clinical manifestations observed in some of the patients.
Hereditary neuropathy or pain disorder v6.37 NFASC Achchuthan Shanmugasundram reviewed gene: NFASC: Rating: GREEN; Mode of pathogenicity: None; Publications: 30850329, 31501903; Phenotypes: Neurodevelopmental disorder with central and peripheral motor dysfunction, OMIM:618356; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Hereditary neuropathy or pain disorder v5.19 NFASC Alexander Rossor gene: NFASC was added
gene: NFASC was added to Hereditary neuropathy or pain disorder. Sources: Expert list
Mode of inheritance for gene: NFASC was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: NFASC were set to 30850329: 30124836
Phenotypes for gene: NFASC were set to Developmental delay; peripheral neuropathy
Penetrance for gene: NFASC were set to Complete
Review for gene: NFASC was set to GREEN
Added comment: Sources: Expert list