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Leber hereditary optic neuropathy v2.9 NSUN3 Neringa Jurkute gene: NSUN3 was added
gene: NSUN3 was added to Leber hereditary optic neuropathy. Sources: Literature
Mode of inheritance for gene: NSUN3 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: NSUN3 were set to PMID: 40465263; PMID: 38790159
Phenotypes for gene: NSUN3 were set to LHON-like phenotype; inherited optic neuropathy; optic atrophy
Mode of pathogenicity for gene: NSUN3 was set to Other
Review for gene: NSUN3 was set to GREEN
Added comment: PMID: 40465263
Biallelic NSUN3 variants were reported to be associated with an early onset severe mitochondrial disorder characterized by combined mitochondrial respiratory chain complex deficiency.
2 individuals from the paper presented with LHON-like phenotype;
5 with attenuated
2 syndromic
Optic atrophy was unifying feature.

PMID: 38790159
Mutations in NSUN3, a Mitochondrial Methyl Transferase Gene, Cause Inherited Optic Neuropathy
Reports early onset optic neuropathy

A follow up par
Sources: Literature