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Intellectual disability v8.105 PLEKHG1 Sarah Leigh Added comment: Comment on publications: PMID: 39202455 was identified by the Genomics England Applied Machine Learning (ML) team in a Biocuration-ML project for identifying new gene-disease associations using Natural Language Processing (NLP) and Generative AI techniques
Intellectual disability v8.105 PLEKHG1 Sarah Leigh Publications for gene: PLEKHG1 were set to 39202455; 30659137
Intellectual disability v8.104 PLEKHG1 Sarah Leigh gene: PLEKHG1 was added
gene: PLEKHG1 was added to Intellectual disability. Sources: Literature
Mode of inheritance for gene: PLEKHG1 was set to MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Publications for gene: PLEKHG1 were set to 39202455; 30659137
Phenotypes for gene: PLEKHG1 were set to Spastic diplegia and psychomotor developmental delay
Review for gene: PLEKHG1 was set to RED
Added comment: PMID: 39202455 reports a de novo heterozygous PLEKHG1 variant (NM_001029884.3 c.370A>G, p.Thr124Ala) in a child with spastic diplegia and psychomotor developmental delay. The child also had cystic fibrosis, due causative CFTR variants inherited from the parents.
A genome-wide association meta-analysis has previously associated the PLEKHG1 locus with white matter hyperintensities (PMID: 30659137).
Sources: Literature