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Cerebral vascular malformations v4.2 SIRT1 Arina Puzriakova Classified gene: SIRT1 as Red List (low evidence)
Cerebral vascular malformations v4.2 SIRT1 Arina Puzriakova Added comment: Comment on list classification: Rating Red as only a single case has been reported to date. Additional evidence is required before attributing causality.
Cerebral vascular malformations v4.2 SIRT1 Arina Puzriakova Gene: sirt1 has been classified as Red List (Low Evidence).
Cerebral vascular malformations v3.26 SIRT1 Alexandra Njegic gene: SIRT1 was added
gene: SIRT1 was added to Cerebral vascular malformations. Sources: Literature
Mode of inheritance for gene: SIRT1 was set to MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Publications for gene: SIRT1 were set to 30578106
Phenotypes for gene: SIRT1 were set to Vein of Galen Malformation
Penetrance for gene: SIRT1 were set to Incomplete
Review for gene: SIRT1 was set to RED
Added comment: 30578106: 1 family, authors identified 1 de novo frameshift SIRT1 variant in proband, proband also harboured a transmitted CLDN14 variant. Supplementary table suggests relatives have capillary malformations.
Sources: Literature