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Early onset or syndromic epilepsy v7.39 SLC13A3 Sarah Leigh Tag Q3_24_promote_green was removed from gene: SLC13A3.
Early onset or syndromic epilepsy v7.39 SLC13A3 Sarah Leigh reviewed gene: SLC13A3: Rating: GREEN; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Early onset or syndromic epilepsy v7.38 SLC13A3 Sarah Leigh Source NHS GMS was added to SLC13A3.
Source Expert Review Green was added to SLC13A3.
Rating Changed from Amber List (moderate evidence) to Green List (high evidence)
Early onset or syndromic epilepsy v7.10 SLC13A3 Arina Puzriakova Tag Q3_24_promote_green tag was added to gene: SLC13A3.
Early onset or syndromic epilepsy v7.10 SLC13A3 Arina Puzriakova Publications for gene: SLC13A3 were set to 38235040; 34966709; 30635937
Early onset or syndromic epilepsy v7.9 SLC13A3 Arina Puzriakova Classified gene: SLC13A3 as Amber List (moderate evidence)
Early onset or syndromic epilepsy v7.9 SLC13A3 Arina Puzriakova Added comment: Comment on list classification: This gene is associated with a relevant phenotype in OMIM (MIM# 618384). At least 9 unrelated cases with biallelic variants in this gene and acute reversible leukoencephalopathy with increased urinary α-ketoglutarate, arising in the context of a febrile illness (PMID: 30635937; 34966709; 35527102; 37290914; 38235040).

Sufficient evidence to promote SLC13A3 to Green at the next GMS panel update.
Early onset or syndromic epilepsy v7.9 SLC13A3 Arina Puzriakova Gene: slc13a3 has been classified as Amber List (Moderate Evidence).
Early onset or syndromic epilepsy v7.8 SLC13A3 Arina Puzriakova Phenotypes for gene: SLC13A3 were changed from to Leukoencephalopathy, acute reversible, with increased urinary alpha-ketoglutarate, OMIM:618384
Early onset or syndromic epilepsy v7.1 SLC13A3 Cassandra Smith gene: SLC13A3 was added
gene: SLC13A3 was added to Early onset or syndromic epilepsy. Sources: Literature
Mode of inheritance for gene: SLC13A3 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: SLC13A3 were set to 38235040; 34966709; 30635937
Review for gene: SLC13A3 was set to GREEN
Added comment: Febrile seizures reported in >3 families with biallelic variants in SLC13A3
Sources: Literature