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Retinal disorders v8.23 SPG11 Achchuthan Shanmugasundram Classified gene: SPG11 as Amber List (moderate evidence)
Retinal disorders v8.23 SPG11 Achchuthan Shanmugasundram Gene: spg11 has been classified as Amber List (Moderate Evidence).
Retinal disorders v8.22 SPG11 Achchuthan Shanmugasundram Added comment: Comment on phenotypes: OMIM phenotype accessed on 29 August 2025.
Retinal disorders v8.22 SPG11 Achchuthan Shanmugasundram Phenotypes for gene: SPG11 were changed from Retinal dystrophy; spastic paraplegia to Spastic paraplegia 11, autosomal recessive, OMIM:604360; retinal disorder, MONDO:0005283
Retinal disorders v8.21 SPG11 Achchuthan Shanmugasundram Publications for gene: SPG11 were set to PMID: 19194956, 36343909, 38613257,21035867
Retinal disorders v8.20 SPG11 Achchuthan Shanmugasundram Tag Q3_25_promote_green tag was added to gene: SPG11.
Tag Q3_25_NHS_review tag was added to gene: SPG11.
Retinal disorders v8.14 SPG11 Ida Ertmanska reviewed gene: SPG11: Rating: GREEN; Mode of pathogenicity: None; Publications: 19194956, 36343909, 38613257, 39391989; Phenotypes: Spastic paraplegia 11, autosomal recessive, OMIM:604360, retinal disorder, MONDO:0005283; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal
Retinal disorders v7.5 SPG11 Siying Lin gene: SPG11 was added
gene: SPG11 was added to Retinal disorders. Sources: Literature
Mode of inheritance for gene: SPG11 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: SPG11 were set to PMID: 19194956, 36343909, 38613257,21035867
Phenotypes for gene: SPG11 were set to Retinal dystrophy; spastic paraplegia
Mode of pathogenicity for gene: SPG11 was set to Other
Review for gene: SPG11 was set to GREEN
Added comment: Kjellin syndrome is a form of complex hereditary spastic paraplegia, associated with 2 genes, SPG11 and SPG15/ZFYVE26. Patients have a consistent retinal phenotype with flecked maculopathy and associated autofluorescence changes. ZFYVE26 is already listed as a green gene on the retinal panel.
Sources: Literature