Activity
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10 actions
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| Primary immunodeficiency or monogenic inflammatory bowel disease v8.82 | TMEFF1 | Ida Ertmanska Tag Q3_25_promote_green was removed from gene: TMEFF1. | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Primary immunodeficiency or monogenic inflammatory bowel disease v8.82 | TMEFF1 | Ida Ertmanska reviewed gene: TMEFF1: Rating: GREEN; Mode of pathogenicity: ; Publications: ; Phenotypes: ; Mode of inheritance: | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Primary immunodeficiency or monogenic inflammatory bowel disease v8.81 | TMEFF1 |
Ida Ertmanska Source NHS GMS was added to TMEFF1. Source Expert Review Green was added to TMEFF1. Rating Changed from Amber List (moderate evidence) to Green List (high evidence) |
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| Primary immunodeficiency or monogenic inflammatory bowel disease v8.55 | TMEFF1 | Achchuthan Shanmugasundram Classified gene: TMEFF1 as Amber List (moderate evidence) | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Primary immunodeficiency or monogenic inflammatory bowel disease v8.55 | TMEFF1 | Achchuthan Shanmugasundram Added comment: Comment on list classification: There is sufficient evidence available (two unrelated cases and functional studies, including mice model) for the promotion of this gene to green rating in the next GMS update. | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Primary immunodeficiency or monogenic inflammatory bowel disease v8.55 | TMEFF1 | Achchuthan Shanmugasundram Gene: tmeff1 has been classified as Amber List (Moderate Evidence). | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Primary immunodeficiency or monogenic inflammatory bowel disease v8.54 | TMEFF1 | Achchuthan Shanmugasundram Tag Q3_25_promote_green tag was added to gene: TMEFF1. | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Primary immunodeficiency or monogenic inflammatory bowel disease v8.54 | TMEFF1 | Achchuthan Shanmugasundram Phenotypes for gene: TMEFF1 were changed from Herpes encephalitis; HSE to encephalitis, acute, infection-induced, susceptibility to, MONDO:0800174 | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Primary immunodeficiency or monogenic inflammatory bowel disease v8.53 | TMEFF1 | Achchuthan Shanmugasundram reviewed gene: TMEFF1: Rating: GREEN; Mode of pathogenicity: None; Publications: 39048823, 39048830; Phenotypes: encephalitis, acute, infection-induced, susceptibility to, MONDO:0800174; Mode of inheritance: BIALLELIC, autosomal or pseudoautosomal | |||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Primary immunodeficiency or monogenic inflammatory bowel disease v6.4 | TMEFF1 |
Boaz Palterer gene: TMEFF1 was added gene: TMEFF1 was added to Primary immunodeficiency or monogenic inflammatory bowel disease. Sources: Literature Mode of inheritance for gene: TMEFF1 was set to BIALLELIC, autosomal or pseudoautosomal Publications for gene: TMEFF1 were set to 39048823; 39048830 Phenotypes for gene: TMEFF1 were set to Herpes encephalitis; HSE Penetrance for gene: TMEFF1 were set to unknown Review for gene: TMEFF1 was set to GREEN Added comment: Chan et al described 2 patients from unrelated kindreds with homozygous LOF variants in TMEFF1 presenting with HSE. Extensive ex vivo and in vitro data, including mice model. Sources: Literature |
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