FAN1

FANCD2 and FANCI associated nuclease 1
OMIM: 613534, Gene2Phenotype

2 panels

Panel Reviews Mode of inheritance Details
2 panels
Green FAN1 in Unexplained kidney failure in young people

Level 3: Disorders of function
Level 2: Renal and urinary tract disorders
Version 1.124

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • Expert list
Phenotypes
  • interstitial nephritis
  • chronic kidney disease
  • Interstitial nephritis, karyomegalic 614817
Green FAN1 in Unexplained young onset end-stage renal disease - additional genes


Level 2: Renal
Version 1.4
Latest signed off version: v1.1 (30 Apr 2025)

Component of the following Super Panels:

  • Unexplained young onset end-stage renal disease
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • Expert Review
    Phenotypes
    • Interstitial nephritis, karyomegalic, OMIM:614817
    • karyomegalic interstitial nephritis, MONDO:0013898
    • chronic kidney disease