GPIHBP1

glycosylphosphatidylinositol anchored high density lipoprotein binding protein 1
OMIM: 612757, Gene2Phenotype

4 panels

Panel Reviews Mode of inheritance Details
4 panels
Green GPIHBP1 in Severe hypertriglyceridaemia

Level 3: Arteriopathies
Level 2: Cardiovascular disorders
Version 1.18

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • UKGTN
  • Eligibility statement prior genetic testing
Phenotypes
  • Hyperlipoproteinemia, type 1D, 615947
Red GPIHBP1 in Familial hypercholesterolaemia

Level 3: Arteriopathies
Level 2: Cardiovascular disorders
Version 1.31

review Not set
Sources
  • Emory Genetics Laboratory
Phenotypes
  • Hypercholesterolemia
Green GPIHBP1 in Familial chylomicronaemia syndrome (FCS)


Level 2: Lipids
Version 3.4
Latest signed off version: v3.0 (22 Mar 2023)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • South West GLH
  • NHS GMS
Phenotypes
  • Hyperlipoproteinemia, type 1D OMIM:615947
  • hyperlipoproteinemia, type 1D MONDO:0014412
Green GPIHBP1 in Likely inborn error of metabolism


Level 2: Metabolic
Version 8.91
Latest signed off version: v8.0 (30 Apr 2025)

Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • NHS GMS
    • Expert Review Green
    • Expert list
    Phenotypes
    • Hyperlipoproteinemia, type 1D OMIM:615947
    • hyperlipoproteinemia, type 1D MONDO:0014412