RASA2

RAS p21 protein activator 2
OMIM: 601589, Gene2Phenotype

4 panels

Panel Reviews Mode of inheritance Details
4 panels
Red RASA2 in Pigmentary skin disorders


Level 2: Dermatology
Version 4.13
Latest signed off version: v4.0 (30 Apr 2025)

review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Other
Phenotypes
  • Noonan syndrome?
Amber RASA2 in RASopathies

Level 3: RASopathies
Level 2: Dysmorphic and congenital abnormality syndromes
Version 1.87

review MONOALLELIC, autosomal or pseudoautosomal, NOT imprinted
Sources
  • Expert Review Amber
  • Other
Phenotypes
  • Noonan syndrome?
Amber RASA2 in Paediatric or syndromic cardiomyopathy


Level 2: Cardiology
Version 7.96
Latest signed off version: v7.0 (30 Apr 2025)

Component of the following Super Panels:

  • Unexplained death in infancy and sudden unexplained death in childhood
  • review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • Expert Review Amber
    • NHS GMS
    • London South GLH
    Phenotypes
    • Noonan syndrome?
    Amber RASA2 in Monogenic short stature


    Level 2: Endocrinology
    Version 1.31
    Latest signed off version: v1.0 (7 Aug 2024)

    review MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
    Sources
    • Expert Review Amber
    • Expert list
    • NHS GMS
    Phenotypes
    • Noonan syndrome