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Adult onset neurodegenerative disorder v9.1 LRSAM1 Oliver Ziff gene: LRSAM1 was added
gene: LRSAM1 was added to Adult onset neurodegenerative disorder. Sources: Literature,Expert Review
Mode of inheritance for gene: LRSAM1 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: LRSAM1 were set to 22781092; 28335037
Phenotypes for gene: LRSAM1 were set to Charcot Marie Toothe disease, axonal, type 2P, 614436
Penetrance for gene: LRSAM1 were set to Complete
Mode of pathogenicity for gene: LRSAM1 was set to Loss-of-function variants (as defined in pop up message) DO NOT cause this phenotype - please provide details in the comments
Review for gene: LRSAM1 was set to GREEN
gene: LRSAM1 was marked as current diagnostic
Added comment: Causes CMT2P with marked motor features out of proportion to sensory loss, presenting as an PMA mimic. Needs inclusion in R460.1 to avoid R78 reanalysis.
Sources: Literature, Expert Review