Activity

Filter

Cancel
Date Panel Item Activity
8 actions
Optic neuropathy v6.46 PHB Eleanor Williams commented on gene: PHB
Optic neuropathy v6.46 PHB Ida Ertmanska Phenotypes for gene: PHB were changed from to optic atrophy, MONDO:0003608
Optic neuropathy v6.45 PHB Ida Ertmanska Classified gene: PHB as Red List (low evidence)
Optic neuropathy v6.45 PHB Ida Ertmanska Added comment: Comment on list classification: As reviewed by Cassandra Smith, there is one pedigree reported in literature where a heterozygous missense variant in PHB1 segregated with optic atrophy. Hence, this gene can only be rated Red until more evidence emerges for the association.
Optic neuropathy v6.45 PHB Ida Ertmanska Gene: phb has been classified as Red List (Low Evidence).
Optic neuropathy v6.44 PHB Ida Ertmanska commented on gene: PHB
Optic neuropathy v6.44 PHB Ida Ertmanska Tag new-gene-name tag was added to gene: PHB.
Optic neuropathy v6.42 PHB Cassandra Smith gene: PHB was added
gene: PHB was added to Optic neuropathy. Sources: Literature
Mode of inheritance for gene: PHB was set to MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Publications for gene: PHB were set to 42067999
Review for gene: PHB was set to AMBER
Added comment: 42067999: c.440C>T (p.Ser147Phe) segregating in five affected members of a three generation family. Ratios of OPA1 short and long isoforms were shifted in patients compared to controls
Sources: Literature