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Ataxia and cerebellar anomalies - narrow panel v8.71 TRMT5 Ida Ertmanska gene: TRMT5 was added
gene: TRMT5 was added to Ataxia and cerebellar anomalies - narrow panel. Sources: Literature
Mode of inheritance for gene: TRMT5 was set to BIALLELIC, autosomal or pseudoautosomal
Publications for gene: TRMT5 were set to 35342985
Phenotypes for gene: TRMT5 were set to Peripheral neuropathy with variable spasticity, exercise intolerance, and developmental delay, OMIM:616539
Review for gene: TRMT5 was set to RED
Added comment: PMID: 35342985 Argente-Escrig et al., 2022
3 cases from apparently unrelated Southern European families with infantile onset demyelinating neuropathy. All compound het for the same TRMT5 variants: [c.312_315del; p.Ile105Serfs*4] and [c.665 T > C; p.Ile222Thr].
The cerebellar ataxia was described as mild (gait disturbance). Neuropathy is the main presentation.
Sources: Literature