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Ataxia and cerebellar anomalies - narrow panel v8.13 ZFHX3 Arina Puzriakova Classified gene: ZFHX3 as Red List (low evidence)
Ataxia and cerebellar anomalies - narrow panel v8.13 ZFHX3 Arina Puzriakova Gene: zfhx3 has been classified as Red List (Low Evidence).
Ataxia and cerebellar anomalies - narrow panel v7.24 ZFHX3_GGC Sarah Leigh edited their review of STR: ZFHX3_GGC: Changed rating: GREEN
Ataxia and cerebellar anomalies - narrow panel v7.24 ZFHX3_GGC Sarah Leigh STR: ZFHX3_GGC was added
STR: ZFHX3_GGC was added to Ataxia and cerebellar anomalies - narrow panel. Sources: Literature
STR, NGS Not Validated tags were added to STR: ZFHX3_GGC.
Mode of inheritance for STR: ZFHX3_GGC was set to MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Phenotypes for STR: ZFHX3_GGC were set to Spinocerebellar ataxia 4, OMIM:600223
Review for STR: ZFHX3_GGC was set to AMBER
Added comment: ZFHX3 transcribed from the reverse strand, which means that the repeated sequence is the reverse compliment of the forward strand sequence.

ZFHX3_GGC is on https://gnomad.broadinstitute.org/short-tandem-repeats?dataset=gnomad_r3

ZFHX3_GGC is on https://stripy.org/database

ZFHX3_GGC is not on DRAGON 4.02.

The coordinates and pathogenic ranges of the sequence repeats were obtained from
https://gnomad.broadinstitute.org/short-tandem-repeats?dataset=gnomad_r3 and were the same on https://stripy.org/database

There is enough evidence for this STR to be green on this panel.

This STR has not been approved by NHS STR working group and is not NGS Not Validated
Sources: Literature
Ataxia and cerebellar anomalies - narrow panel v4.58 ZFHX3 Dmitrijs Rots reviewed gene: ZFHX3: Rating: RED; Mode of pathogenicity: None; Publications: ; Phenotypes: ; Mode of inheritance: None
Ataxia and cerebellar anomalies - narrow panel v4.58 ZFHX3 Sarah Leigh reviewed gene: ZFHX3: Rating: AMBER; Mode of pathogenicity: None; Publications: ; Phenotypes: ; Mode of inheritance: None
Ataxia and cerebellar anomalies - narrow panel v4.58 ZFHX3 Sarah Leigh Tag STR tag was added to gene: ZFHX3.
Ataxia and cerebellar anomalies - narrow panel v4.58 ZFHX3 Sarah Leigh Phenotypes for gene: ZFHX3 were changed from syndromic intellectual disability to Spinocerebellar ataxia 4, OMIM:600223; spinocerebellar ataxia type 4, MONDO:0010847
Ataxia and cerebellar anomalies - narrow panel v4.57 ZFHX3 Sarah Leigh Entity copied from Intellectual disability - microarray and sequencing v5.499
Ataxia and cerebellar anomalies - narrow panel v4.57 ZFHX3 Sarah Leigh gene: ZFHX3 was added
gene: ZFHX3 was added to Ataxia and cerebellar anomalies - narrow panel. Sources: Expert Review Amber,Literature
Mode of inheritance for gene: ZFHX3 was set to MONOALLELIC, autosomal or pseudoautosomal, imprinted status unknown
Publications for gene: ZFHX3 were set to 38412861; 38035881; 37292950
Phenotypes for gene: ZFHX3 were set to syndromic intellectual disability