AMPD1

adenosine monophosphate deaminase 1
OMIM: 102770, Gene2Phenotype

4 panels

Panel Reviews Mode of inheritance Details
4 panels
Green AMPD1 in Rhabdomyolysis and metabolic muscle disorders


Level 2: Neurology
Version 5.14
Latest signed off version: v5.4 (30 Apr 2025)

Component of the following Super Panels:

  • Hypotonic infant
  • Other rare neuromuscular disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • NHS GMS
    • Illumina TruGenome Clinical Sequencing Services
    • Radboud University Medical Center, Nijmegen
    • Emory Genetics Laboratory
    Phenotypes
    • Myopathy due to myoadenylate deaminase deficiency, OMIM:615511
    Tags
    • Q3_25_expert_review
    • Q3_25_demote_red
    Red AMPD1 in Undiagnosed metabolic disorders

    Level 3: Specific metabolic abnormalities
    Level 2: Metabolic disorders
    Version 1.642

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Red
    • Literature
    Phenotypes
    • Myoadenylate deaminase deficiency (Disorders of purine metabolism)
    • Myopathy due to myoadenylate deaminase deficiency 615511
    Red AMPD1 in Likely inborn error of metabolism


    Level 2: Metabolic
    Version 8.91
    Latest signed off version: v8.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • London North GLH
    • NHS GMS
    • Expert Review Red
    Phenotypes
    • Myoadenylate deaminase deficiency (Disorders of purine metabolism)
    • Myopathy due to myoadenylate deaminase deficiency 615511
    Green AMPD1 in Acute rhabdomyolysis


    Level 2: Neurology
    Version 2.7
    Latest signed off version: v2.0 (30 Apr 2025)

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • NHS GMS
    Phenotypes
    • Myopathy due to myoadenylate deaminase deficiency, OMIM:615511
    Tags
    • Q3_25_expert_review
    • Q3_25_demote_red