SLC6A20

solute carrier family 6 member 20
OMIM: 605616, Gene2Phenotype

5 panels

Panel Reviews Mode of inheritance Details
5 panels
Red SLC6A20 in Familial Hirschsprung Disease

Level 3: Gastrointestinal disorders
Level 2: Gastroenterological disorders
Version 1.11

review Unknown
Sources
  • Expert Review Red
  • Literature
Phenotypes
  • risk of HSCR
Red SLC6A20 in Nephrocalcinosis or nephrolithiasis


Level 2: Renal
Version 5.5
Latest signed off version: v5.0 (30 Apr 2025)

Component of the following Super Panels:

  • Unexplained young onset end-stage renal disease
  • review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
    Sources
    • Expert
    Red SLC6A20 in Undiagnosed metabolic disorders

    Level 3: Specific metabolic abnormalities
    Level 2: Metabolic disorders
    Version 1.642

    review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
    Sources
    • Expert Review Red
    • UKGTN
    • Illumina TruGenome Clinical Sequencing Services
    • Literature
    • Radboud University Medical Center, Nijmegen
    Phenotypes
    • Hyperglycinuria 138500
    • Iminoglycinuria, digenic 242600
    Tags
    • refuted
    Red SLC6A20 in Likely inborn error of metabolism


    Level 2: Metabolic
    Version 8.91
    Latest signed off version: v8.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review BOTH monoallelic and biallelic, autosomal or pseudoautosomal
    Sources
    • NHS GMS
    • Expert Review Red
    Phenotypes
    • Hyperglycinuria
    Tags
    • gene-checked
    • refuted
    Red SLC6A20 in Childhood onset dystonia, chorea or related movement disorder


    Level 2: Neurology
    Version 7.13
    Latest signed off version: v7.0 (30 Apr 2025)

    review Not set
    Sources
    • Expert Review Red
    • London North GLH