XYLT2

xylosyltransferase 2
OMIM: 608125, Gene2Phenotype

9 panels

Panel Reviews Mode of inheritance Details
9 panels
Green XYLT2 in Congenital disorders of glycosylation


Level 2: Metabolic
Version 7.16
Latest signed off version: v7.0 (30 Apr 2025)

Component of the following Super Panels:

  • Hereditary ataxia and cerebellar anomalies - childhood onset
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • Radboud University Medical Center, Nijmegen
    • Literature
    Phenotypes
    • Spondyloocular syndrome 605822
    Green XYLT2 in Bilateral congenital or childhood onset cataracts


    Level 2: Ophthalmology
    Version 7.10
    Latest signed off version: v7.0 (30 Apr 2025)

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert list
    • Expert Review Green
    Phenotypes
    • Spondyloocular syndrome, 605822
    Red XYLT2 in Rare genetic inflammatory skin disorders


    Level 2: Dermatology
    Version 4.18
    Latest signed off version: v4.0 (30 Apr 2025)

    review Not set
    Sources
    • London North GLH
    • Expert Review Red
    • NHS GMS
    Phenotypes
    • Scleroderma
    Green XYLT2 in Skeletal dysplasia


    Level 2: Musculoskeletal
    Version 8.40
    Latest signed off version: v8.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • NHS GMS
    • Expert Review Green
    • Expert list
    Phenotypes
    • Spondyloocular syndrome 605822
    Green XYLT2 in Undiagnosed metabolic disorders

    Level 3: Specific metabolic abnormalities
    Level 2: Metabolic disorders
    Version 1.645

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    Phenotypes
    • Spondyloocular syndrome
    Green XYLT2 in Likely inborn error of metabolism


    Level 2: Metabolic
    Version 8.107
    Latest signed off version: v8.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    Phenotypes
    • Spondyloocular syndrome
    Green XYLT2 in Fetal anomalies


    Level 2: Fetal (including NIPD)
    Version 6.185
    Latest signed off version: v6.0 (30 Apr 2025)

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • PAGE DD-Gene2Phenotype
    Phenotypes
    • SPONDYLOOCULAR SYNDROME
    Green XYLT2 in DDG2P


    Version 6.447
    Latest signed off version: v6.0 (30 Apr 2025)

    Component of the following Super Panels:

  • Paediatric disorders
  • review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • DD-Gene2Phenotype
    Phenotypes
    • SPONDYLOOCULAR SYNDROME 605822
    Red XYLT2 in Childhood onset dystonia, chorea or related movement disorder


    Level 2: Neurology
    Version 7.20
    Latest signed off version: v7.0 (30 Apr 2025)

    review Not set
    Sources
    • Expert Review Red
    • London North GLH