PDXK

pyridoxal kinase
OMIM: 179020, Gene2Phenotype

4 panels

Panel Reviews Mode of inheritance Details
4 panels
Green PDXK in Optic neuropathy


Level 2: Ophthalmology
Version 5.48
Latest signed off version: v5.0 (30 Apr 2025)

review BIALLELIC, autosomal or pseudoautosomal
Sources
  • Expert Review Green
  • NHS GMS
  • Literature
Phenotypes
  • Neuropathy, hereditary motor and sensory, type VIC, with optic atrophy, OMIM:618511
Red PDXK in Undiagnosed metabolic disorders

Level 3: Specific metabolic abnormalities
Level 2: Metabolic disorders
Version 1.642

review Unknown
Sources
  • Expert Review Red
  • Literature
Phenotypes
  • Pryridoxal kinase deficiency (Disorders of pyridoxine metabolism)
Red PDXK in Likely inborn error of metabolism


Level 2: Metabolic
Version 8.91
Latest signed off version: v8.0 (30 Apr 2025)

Component of the following Super Panels:

  • Childhood onset leukodystrophy
  • Hypotonic infant
  • Paediatric disorders
  • Unexplained death in infancy and sudden unexplained death in childhood
  • review Unknown
    Sources
    • London North GLH
    • NHS GMS
    • Expert Review Red
    Phenotypes
    • Pryridoxal kinase deficiency (Disorders of pyridoxine metabolism)
    Green PDXK in Hereditary neuropathy or pain disorder


    Level 2: Neurology
    Version 7.36
    Latest signed off version: v7.0 (30 Apr 2025)

    review BIALLELIC, autosomal or pseudoautosomal
    Sources
    • Expert Review Green
    • NHS GMS
    • Literature
    Phenotypes
    • Neuropathy, hereditary motor and sensory, type VIC, with optic atrophy, OMIM:618511